Prune Belly Syndrome Network Website for the prune belly syndrome Network The PBSN is a nonprofit organization devoted to health education, information and support for the person with http://www.prunebelly.org/
Extractions: Send comments or questions to webmaster@prunebelly.org Welcome! Here you will find a collection of information about Prune Belly Syndrome which is also known as Eagle-Barrett Syndrome. The Prune Belly Syndrome Network, Inc. provides support for those who have Prune Belly, their families, friends and the health care professionals who treat them. NEW! Convention News!
Extractions: About Prune Belly ... Links Also known as Eagle-Barrett syndrome, the Prune Belly syndrome consists of a triad of features: Anterior abdominal wall: musculature is deficient or absent. Urinary tract anomalies (mega-ureters, large bladder). Bilateral cryptorchidism (undescended testicles). The incidence of prune belly syndrome is 1 in 40,000 live births; 95% of cases occur in males. In the past, it was suggested that the abdominal wall was deformed by pressure from a distended bladder due to bladder outlet obstruction in utero. Currently it is thought that prune belly syndrome is a multisystem disease complex which derives from a primary defect in mesodermal development. The major prognostic factor is the degree of dilation of the urinary tract; 20% of patients are stillborn, 30% die of renal failure or urosepsis within the first two years of life, and the remaining 50% have varying degrees of urinary pathology. Renal abnormalities vary widely. There may be agenesis or hypoplasia, which is rare, or hydronephrosis. On IVP, 80% of patients have evident tortuous ureters with dilatation distally. Vesicoureteral reflux is common. The bladder is generally dilated, and the trabecula are thinned. A patent urachus may allow the bladder to decompress.
Prune Belly Syndrome Management of the child with prune belly syndrome (PBS) has posed a significant amount of trouble to the to see is that prune belly syndrome can present with a spectrum http://www.pedsurology.com/prune.htm
Extractions: Prune Belly Syndrome INTRODUCTION Management of the child with prune belly syndrome (PBS) has posed a significant amount of trouble to the pediatric urologist. There have been calls for conservative management of the urinary tract in these boys by some authors while others have advocated an aggressive approach to the management of these patients, operating on them at ten days of life. At the present time, no definitive timing for therapy has been substantiated one way or the other. What we have been able to see is that prune belly syndrome can present with a spectrum of abnormalities ranging from the stillborn infant with severe urogenital and pulmonary problems to the child with little, if any, urological abnormalities requiring no therapy other than orchidopexies to correct the undescended testes. It appears that the decision to intervene in the management of the urinary tract of these children should be based on the clinical presentation and not solely on radiographic appearance. There is little controversy in the literature as to the present management of the undescended testes in these children. If controversy or confusion arises, it is to the optimal timing for the surgery for the orchidopexy as well the type of orchidopexy to be performed. Similarly, the management of the abdominal wall abnormalities has several camps with some going for no surgical reconstruction of the abdominal wall while others advocate surgical reconstruction and this group being divided amongst two separate factions advocating different techniques of abdominal wall reconstruction.
Prune Belly Syndrome prune belly syndrome. National prune belly syndrome Association. 30 Salem Blvd The National Organization for Rare Disorders prune belly syndrome information http://www.kumc.edu/gec/support/prunbely.html
Prune Belly Syndrome / Family Village Library prune belly syndrome. Synonym EagleBarrett Syndrome. Who to Contact. Where to Go to Chat with Others. Learn More About It. Web Sites. Search Google for "prune belly syndrome" Who to Contact. Prune http://www.familyvillage.wisc.edu/lib_prune-belly.html
Extractions: A list for parents and caregivers of children with Posterior Urethral Valves (or other obstructive uropathy). We also welcome members who have children with prune belly syndrome, VATERS, or other congenital urologic or kidney anomoly. Whether the child has been born yet or not, whether the child lived or not, whether the child had kidney/urinary track problems or not....everyone is welcome to be part of the PUVs family. What is Prune Belly Syndrome?
Extractions: (advertisement) Home Specialties CME PDA ... Patient Education Articles Images CME Patient Education Advanced Search Link to this site Back to: eMedicine Specialties Radiology Pediatrics Last Updated: December 7, 2001 Rate this Article Email to a Colleague Synonyms and related keywords: congenital absence of abdominal musculature, deficiency of abdominal musculature, Eagle-Barrett syndrome, triad syndrome AUTHOR INFORMATION Section 1 of 10 Author Information Introduction Differentials X-ray ... Bibliography Author: Beverly P Wood, MD, MS , Professor, Departments of Radiology and Pediatrics, Division of Medical Education, Keck School of Medicine, University of Southern California Beverly P Wood, MD, MS, is a member of the following medical societies: American Academy of Pediatrics American Association for Women Radiologists American College of Radiology American Institute of Ultrasound in Medicine ... American Roentgen Ray Society , Association of University Radiologists, Radiological Society of North America , and Society for Pediatric Radiology Editor(s): Robert J Starshak, MD
MedlinePlus Medical Encyclopedia: Prune Belly Syndrome prune belly syndrome. Definition Return to top. prune belly syndrome is a group of congenital anomalies characterized by three major findings http://www.nlm.nih.gov/medlineplus/ency/article/001269.htm
Extractions: @import url(http://www.nlm.nih.gov/medlineplus/images/advanced.css); Skip navigation Other encyclopedia topics: A-Ag Ah-Ap Aq-Az B-Bk ... Z Contents of this page: Abdominal muscles Alternative names Return to top Eagle-Barrett syndrome Definition Return to top Prune belly syndrome is a group of congenital anomalies characterized by three major findings: Causes, incidence, and risk factors Return to top The underlying causes of prune belly syndrome are unknown. 96-97% of cases are boys. Expectant mothers carrying affected infants may develop varying degrees of oligohydramnios (insufficient amniotic fluid ) that make it likely the infant will have lung problems. (See also Potter syndrome The newborn infant has a wrinkled abdomen that looks like a prune. This is because the abdomen swelled with fluid in the womb, then lost that fluid after birth, leading to wrinkles of excess skin. The appearance is accentuated by the lack of adequate abdominal musculature. Many infants are either stillborn or die within the first few weeks of life from severe lung or kidney problems, or a combination of congenital anomalies.
Pediatric Database Offers a definition of prune belly syndrome, the epidemiology, pathogenesis, pathology, clinical features, investigations and management. http://www.icondata.com/health/pedbase/files/PRUNEBEL.HTM
Medical Encyclopedia: Prune Belly Syndrome (Print Version) Medical Encyclopedia prune belly syndrome. Definition. prune belly syndrome is a group of congenital anomalies characterized by three major findings http://www.nlm.nih.gov/medlineplus/print/ency/article/001269.htm
Extractions: To close this window, click on the "x" in the upper right hand corner of the window. URL of this page: http://www.nlm.nih.gov/medlineplus/ency/article/001269.htm Alternative names Eagle-Barrett syndrome Definition Prune belly syndrome is a group of congenital anomalies characterized by three major findings: Causes, incidence, and risk factors The underlying causes of prune belly syndrome are unknown. 96-97% of cases are boys. Expectant mothers carrying affected infants may develop varying degrees of oligohydramnios (insufficient amniotic fluid) that make it likely the infant will have lung problems. (See also Potter syndrome.) The newborn infant has a wrinkled abdomen that looks like a prune. This is because the abdomen swelled with fluid in the womb, then lost that fluid after birth, leading to wrinkles of excess skin. The appearance is accentuated by the lack of adequate abdominal musculature. Many infants are either stillborn or die within the first few weeks of life from severe lung or kidney problems, or a combination of congenital anomalies. Symptoms Signs and tests Oligohydramnios (decreased or absent amniotic fluid) Dilated renal collecting structures
Extractions: (advertisement) Home Specialties CME PDA ... Patient Education Articles Images CME Patient Education Advanced Search Link to this site Back to: eMedicine Specialties Medicine, Ob/Gyn, Psychiatry, and Surgery Urology Last Updated: August 24, 2001 Rate this Article Email to a Colleague Synonyms and related keywords: PBS, Eagle-Barrett syndrome, triad syndrome AUTHOR INFORMATION Section 1 of 11 Author Information Introduction Indications Relevant Anatomy And Contraindications ... Bibliography Author: Israel Franco, MD , Associate Professor, Departments of Urology, Division of Pediatric Urology, New York Medical College Israel Franco, MD, is a member of the following medical societies: American Academy of Pediatrics American College of Surgeons American Urological Association Endourological Society ... Medical Society of the State of New York , and Society of Laparoendoscopic Surgeons Editor(s): Peter Langenstroer, MD , Assistant Professor, Department of Surgery, Division of Urology, Medical College of Wisconsin; Francisco Talavera, PharmD, PhD
Prune Belly (Eagle-Barrett) Syndrome prune belly syndrome, also known as EagleBarrett or triad syndrome, is a distinctive set of physical problems that a child is born with. prune belly syndrome. http://rarediseases.about.com/cs/prunebellysynd/a/032302.htm
Extractions: zJs=10 zJs=11 zJs=12 zJs=13 zc(5,'jsc',zJs,9999999,'') About Rare / Orphan Diseases Home Essentials ... Rare cancers zau(256,152,145,'gob','http://z.about.com/5/ad/go.htm?gs='+gs,''); Is it a Rare Disease? Rare Diseases A - B Rare Diseases C - D Rare Diseases E - H ... Help zau(256,138,125,'el','http://z.about.com/0/ip/417/0.htm','');w(xb+xb); Subscribe to the About Rare / Orphan Diseases newsletter. zau(256,152,100,'hs','http://z.about.com/5/ad/hs.htm?zIhsid=00',''); Search Rare / Orphan Diseases Email to a friend Print this page Stay Current Subscribe to the About Rare / Orphan Diseases newsletter. Suggested Reading Internet links on Prune Belly syndrome Elsewhere on the Web Prune Belly Syndrome Network Most Popular ALD and Lorenzo's Oil The Elephant Man's Bones Reveal Mystery Prune Belly (Eagle-Barrett) Syndrome Progeria Syndromes ... Mad Cow Disease and Humans What's Hot Autoimmune Kidney Disease Tourette Syndrome Christmas Disease Bugs, PANDAS, and Tics ... Dystonia and Botox Injections From Mary Kugler
Prune Belly (Eagle-Barrett) Syndrome Diseases newsletter. Suggested Reading. Internet links on prune belly syndrome. Elsewhere on the Web. prune belly syndrome Network. http://rarediseases.about.com/library/weekly/aa032302a.htm
Extractions: zJs=10 zJs=11 zJs=12 zJs=13 zc(5,'jsc',zJs,9999999,'') About Rare / Orphan Diseases Home Essentials ... Rare cancers zau(256,152,145,'gob','http://z.about.com/5/ad/go.htm?gs='+gs,''); Is it a Rare Disease? Rare Diseases A - B Rare Diseases C - D Rare Diseases E - H ... Help zau(256,138,125,'el','http://z.about.com/0/ip/417/0.htm','');w(xb+xb); Subscribe to the About Rare / Orphan Diseases newsletter. zau(256,152,100,'hs','http://z.about.com/5/ad/hs.htm?zIhsid=00',''); Search Rare / Orphan Diseases Email to a friend Print this page Stay Current Subscribe to the About Rare / Orphan Diseases newsletter. Suggested Reading Internet links on Prune Belly syndrome Elsewhere on the Web Prune Belly Syndrome Network Most Popular ALD and Lorenzo's Oil The Elephant Man's Bones Reveal Mystery Prune Belly (Eagle-Barrett) Syndrome Progeria Syndromes ... Mad Cow Disease and Humans What's Hot Autoimmune Kidney Disease Tourette Syndrome Christmas Disease Bugs, PANDAS, and Tics ... Dystonia and Botox Injections From Mary Kugler
Extractions: Web Directory: NORD: Prune Belly Syndrome Offers a list of synonyms, a general discussion and further resources. Pediatric Database Offers a definition of Prune Belly Syndrome, the epidemiology, pathogenesis, pathology, clinical features, investigations and management. Prune Belly Syndrome Network Devoted to health education, information and support for the person with the condition as well as their friends, families or the health professionals who treat them. Also known as Eagle-Barrett syndrome.
Prune Belly Syndrome - Lucile Packard Children's Hospital Genitourinary Kidney Disorders. prune belly syndrome What is prune belly syndrome? Prune What causes prune belly syndrome? Prune http://www.lpch.org/DiseaseHealthInfo/HealthLibrary/urology/pbs.html
Extractions: What is prune belly syndrome? Prune belly syndrome is also known as triad syndrome or Eagle-Barrett syndrome. It is characterized by a triad of abnormalities that include the following: Because of the substantial involvement of the urinary tract, children with prune belly syndrome are usually unable to completely empty their bladders and have serious bladder, ureter, and kidney impairment. A child with prune belly syndrome may also have other birth defects. Most commonly, these defects involve the skeletal system, intestines, and heart. Girls may have defects in their external genitalia, as well. Some infants who have prune belly syndrome may be stillborn or die within a few months of birth.
AllRefer Health - Prune Belly Syndrome (Eagle-Barrett Syndrome) prune belly syndrome (EagleBarrett Syndrome) information center covers causes, prevention, symptoms, diagnosis, treatment, incidence, risk factors, signs http://health.allrefer.com/health/prune-belly-syndrome-info.html
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Extractions: AllRefer Channels :: Yellow Pages Reference Health Home ... Contact Us Quick Jump ADD/ADHD Allergies Alzheimer's Disease Arthritis Asthma Back Pain Breast Cancer Cancer Colon Cancer Depression Diabetes Gallbladder Disease Heart Attack Hepatitis High Cholesterol HIV/AIDS Hypertension Lung Cancer Menopause Migraines/Headaches Osteoporosis Pneumonia Prostate Cancer SARS Stroke Urinary Tract Infection 1600+ More Conditions Alternative Medicine Health News Symptoms Guide Special Topics ... Medical Encyclopedia
